Papillon lefevre syndrome- A literature review and case report
نویسندگان
چکیده
منابع مشابه
Papillon–Lefevre Syndrome: A Case Report with Review of Literature
papillon-Lefèvre Syndrome (PLS) Is A Very Rare Autosomal Recessive Disorder Characterized By Palmoplantar Hyperkeratosis And Severe Early Onset Of Destructive Periodontitis Leading To Premature Loss Of Both Primary And Permanent Dentitions. Here We Are Presenting Case Report Of Siblings Who Presented With Palmoplantar Hyperkeratosis And Aggressive Periodontitis.
متن کاملPapillon-Lefevre Syndrome: A Case Report
PapillonLefevre syndrome (PLS) is a very rare autosomal recessive disorder characterized by palmoplantar hyperkeratosis and severe early onset of destructive periodontitis leading to premature loss of both primary and permanent dentition.PLS is transmitted as an autosomal recessive condition and consanguinity of parents is evident in about one third of cases. Here we report a case of a 13 year ...
متن کاملPapillon-Lefevre syndrome: a case report.
Papillon-Lefevre syndrome is a rare autosomal recessive genetic disorder. The clinical manifestations include palmer planter hyperkeratosis with precocious progressive periodontal disease that results in premature exfoliation of primary and permanent dentitions. Patients are often edentulous at an early age. This is a case report of prosthodontic rehabilitation of a 15-year-old girl with Papill...
متن کاملPapillon-Lefevre Syndrome Causing Social Stigma – A Case Report and Review
Background: Papillon-Lefevre syndrome is a rare autosomal recessive genetic disorder which is characterized by palmar plantar hyperkeratosis with precocious progressive periodontal disease that results in premature exfoliation of primary and permanent dentitions. Consanguinity of parents is evident in about one third of cases. Context: Here we report a case of 22 year old male who presented wit...
متن کاملPapillon Lefevre syndrome.
Papillon Lefèvre syndrome is a rare disease characterized by skin lesions caused by palmar-plantar hyperkeratosis, and severe periodontal destruction involving both the primary and permanent dentitions. It is transmitted as an autosomal recessive condition and consanguinity of parents is evident in about one-third of cases. Pyogenic liver abscess is an increasingly recognized complication. We r...
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ژورنال
عنوان ژورنال: IP International Journal of Periodontology and Implantology
سال: 2019
ISSN: 2581-9836,2457-0087
DOI: 10.18231/j.ijpi.2019.023